- Metabolite
- HMDB0000491 (3-Methyl-2-oxovaleric acid)
- Biospecimen
- Urine
- Status
- Detected and Quantified
- Data source
- Referenced
- Concentration
- 209.0 +/- 35.0 umol/mmol creatinine
- Age
- Adult (>18 years old)
- Sex
- Both
- Condition
- Maple syrup urine disease (MSUD)
References
- Schadewaldt P, Hammen HW, Ott AC, Wendel U: Renal clearance of branched-chain L-amino and 2-oxo acids in maple syrup urine disease. J Inherit Metab Dis. 1999 Aug;22(6):706-22. [PubMed:10472531 ]